Abstract

Congenital nasal lesions (such as nasal dermoid, encephalocele, and gliomas) are rare and result from abnormal embryonic development. It is necessary to distinguish them and understand their full pathology to avoid unnecessary complications. Nasal dermoid cyst-like swelling is a rare ectodermal and mesodermal origin condition, with a connecting tube or tail extending intra-cranially in only 10% of congenital diseases. The intracranial component of the mass predisposes children to meningitis and abscess formation. Another swelling, such as craniofacial neurofibromatosis, is a benign but devastating disease often accompanied by significant mid-face deformity. Recurrence can be seen if inadequately removed, so all patients' long-term follow-up should be done.Here we present a case of midline nasal swelling in a 1-year-old child and share our experience about the successful management of midline nasal mass.