Abstract

Partial anomalous pulmonary venous connection (PAPVC) is a rare congenital anomaly often associated with sinus venosus atrial septal defect (SVASD). We report a unique case of a 4-year-old male presenting with dyspnea on exertion, diagnosed with right-sided PAPVC involving all three right pulmonary veins draining into the right atrium (RA), an inferior SVASD, and anomalous inferior vena cava (IVC) drainage into the left atrium (LA). Diagnosis was confirmed with echocardiography and CT imaging. Surgical correction involved rerouting the anomalous venous connections using a Dacron patch and augmenting the IVC-RA junction with a pericardial patch. The patient had an uneventful recovery. This case highlights the importance of precise imaging, thorough anatomical understanding, and tailored surgical techniques in managing rare and complex congenital heart defects.