Abstract

Vulval sarcomas account for only 1-3% of all vulval malignancies. Common vulval sarcomas described are Leiomyosarcoma, Angiomyxoma, fibrohistosarcoma. Malignant extra renal rhabdoid (ERT/MRT) of vulva is very rare and very aggressive neoplasm with very poor prognosis. Median survival reported in studies is 9 months to 61 months. Only 14 cases have been reported till date in English literature. We are reporting the 15th very rare case of a 31 years young female with primary vulval extra renal rhabdoid tumour of vulva who presented with tender vulval swelling with a short duration of 15 days.