Abstract

Introduction: Rhabdomyosarcoma accounts for up to 60% of childhood soft tissue sarcoma, occurring mostly in the head and neck region but rarely in the ear and temporal areas. Case Report: A 4-year-old boy symptomaticaly treated at rural center for 3-4 months and then referred to our hospital due to a purulent discharge. Also seen mass in the right external auditory canal along with facial deviation to the left side. After histopathologic evaluation, it was diagnosed as embryonal rhabdomyosarcoma. Conclusion: Rhabdomyosarcoma should be kept in mind as a differential diagnosis in all children presenting with chronic otitis media (CSOM). Biopsy should be considered who are not responding to medications and those worsening condition.