Journal of Neonatal Research and Pediatric Care ISSN: 2691-5901
Case Report
Extreme Reduction of Serum Uric Acid in Patients with Lesch-Nyhan Disease: Reduction of Nephrolithiasis
Published: 2019-10-22

Abstract

Lesch-Nyhan disease (LND) or Lesch-Nyhan Syndrome (LNS) is an X-linked recessive disorder of the purine salvage pathway in which hyperuricemia, is associated with gout and uric acid nephrolithiasis. It is also characterized by cognitive impairment, dystonia and dramatic behavioral manifestations, including the hallmark self-injurious behaviors.

Keywords

Lesch-Nyhan disease; Lesch-Nyhan Syndrome; Nephrolithiasis; Dystonia