Abstract

Myotonic dystrophy is the most common muscular dystrophy seen in adults, which can affect the heart, brain, gastrointestinal tract, and other non-muscular organs. Patients with myotonic dystrophy can develop a range of cardiac abnormalities, including conduction abnormalities, dilated cardiomyopathy, arrhythmias, mitral valve prolapse, myocardial dysfunction, and ischemic heart disease. In this case report, we describe a patient with type 1 myotonic dystrophy, who underwent coronary artery bypass grafting and closure of atrial septal defect. We discuss the challenges experienced during the perioperative period and the management which led to a successful outcome.